Absence of Spleen

A Case of Congenital Absence of the Spleen

Syndrome of Congenital Absence of the Spleen with Associated Cardiovascular and Gastroenteric Anomalies

Survey of 27 cases in the literature and the authors' 3 cases reveals a characteristic syndrome of congenital absence of the spleen with certain cardiovascular and gastrointestinal abnormalities. The hematologic and other findings permit a presumptive antemortem diagnosis. More accurate prognosis is made possible and valuable information is afforded the cardiac surgeon, since the cardiac anomal...

Report of a case with congenital absence of the spleen and laevocardia.

Congenital absence of the spleen is a rare anomaly. The first case to be described in infancy is that of Martin (1826). At necropsy a partial situs inversus of the viscera and congenital malformations of the heart were found. Polhemus and Schafer (1952) reviewed the literature up to 1952 and found 12 cases of congenital absence of the spleen in infants. To these they added four cases of their o...

Congenital malformations of the heart and the great vessels associated with congenital absence of the spleen.

The unusual combination of congenital malformations of the heart and great vessels on the one hand, with agenesis of the spleen on the other hand has been looked upon as a great medical curiosity. In the past it had been the pathologist exclusively who from time to time encountered this association of anomalies. More recently, however, cases have been diagnosed by the clinician during the life ...

Syndrome of congenital absence of the spleen with associated cardiovascular and gastroenteric anomalies.

Survey of 27 cases in the literature and the authors' 3 cases reveals a characteristic syndrome of congenital absence of the spleen with certain cardiovascular and gastrointestinal abnormalities. The hematologic and other findings permit a presumptive antemortem diagnosis. More accurate prognosis is made possible and valuable information is afforded the cardiac surgeon, since the cardiac anomal...